Gonadotrophin-releasing hormone pulse generator (arcuate nucleus)

Hypothalamus · GnRH Kisspeptin Pulsatile

KNDy (kisspeptin, neurokinin B, dynorphin) neurones of the arcuate nucleus pace GnRH into the portal blood roughly every 60-90 minutes. The frequency, not the amount, decides whether LH or FSH dominates.

Detail

Pulse code
Fast pulses favour LH-beta transcription, slow pulses favour FSH-beta; continuous exposure desensitises the gonadotroph
Therapeutic use
Continuous GnRH agonist (goserelin, leuprorelin) gives an initial flare then medical castration in prostate cancer and endometriosis; pulsatile GnRH by pump restores fertility in hypothalamic disease
Restrained by
Prolactin, low energy availability and leptin, opioids, glucocorticoids; progesterone slows the pulse

When it goes wrong

Kallmann syndrome — failed migration of GnRH neurones with the olfactory placode

Hypogonadotrophic hypogonadism with anosmia: absent puberty, low LH, FSH and testosterone; gonadotrophins or pulsatile GnRH are needed for fertility

Functional hypothalamic amenorrhoea from low body weight, heavy training or stress

Slowed pulses give low LH and FSH with low oestradiol: secondary amenorrhoea, negative pregnancy test, normal prolactin and low bone density

GnRH agonist started for metastatic prostate cancer without antiandrogen cover

Testosterone flare in the first fortnight worsening bone pain or causing spinal cord compression

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