Hypercalcaemia of malignancy

Effect · PTHrP PTH suppressed

The commonest cause of hypercalcaemia in inpatients and the diagnosis to reach for when PTH is suppressed. Three mechanisms: PTHrP acting at the PTH1R, osteolytic metastases, and unregulated 1-alpha-hydroxylation in lymphoma.

Traced from the start

  1. Fall in ionised calciumRise in ionised calcium
  2. Calcium-sensing receptor on parathyroid chief cells
  3. Thyroid parafollicular (C) cells
  4. Parathyroid hormoneCalcitonin
  5. Bone: osteoblast-osteoclast couplingDistal convoluted and connecting tubule: calcium reabsorption
  6. Hypercalcaemia of malignancy

Detail

Humoral (PTHrP)
Squamous cell carcinoma of lung, head and neck or oesophagus, renal cell carcinoma and breast carcinoma; PTHrP acts at PTH1R, so phosphate is low as in primary hyperparathyroidism, but PTH is suppressed and calcitriol is low
Osteolytic
Myeloma and breast carcinoma metastases, through locally produced cytokines and RANKL
Calcitriol-mediated
Hodgkin and non-Hodgkin lymphoma, by the same unregulated macrophage 1-alpha-hydroxylation as granulomatous disease
Discriminator
A suppressed PTH points away from primary hyperparathyroidism; measure PTHrP if the cause is not already obvious
Treatment
Intravenous 0.9% sodium chloride, then zoledronic acid; denosumab if bisphosphonate-refractory or in renal impairment; corticosteroids for the calcitriol-mediated forms

When it goes wrong

Hypercalcaemia with a suppressed PTH in a smoker with a lung mass

Humoral hypercalcaemia of malignancy from PTHrP; it carries a poor prognosis

Hypercalcaemia with anaemia, renal impairment and back pain

Myeloma: request serum protein electrophoresis, serum free light chains and imaging for lytic lesions

Practise this structure

2 questions in the bank tagged Ionised Calcium.