Hypopituitarism and the order in which axes fail

Effect and feedback · GH first ACTH last Steroid before thyroxine

When the anterior pituitary is compressed or infarcted the axes usually fail in a set order: growth hormone, then the gonadotrophins, then TSH, then ACTH. Prolactin is lost last, or is raised instead when the stalk is involved.

Traced from the start

  1. Corticotrophin-releasing hormone (paraventricular nucleus)
  2. Corticotroph — ACTH cleaved from pro-opiomelanocortin
  3. Adrenal cortex — zona fasciculata and zona reticularis
  4. Thyrotrophin-releasing hormone (paraventricular nucleus)
  5. Thyrotroph — thyroid-stimulating hormone
  6. Thyroid follicular cell
  7. Gonadotrophin-releasing hormone pulse generator (arcuate nucleus)
  8. Gonadotroph — luteinising hormone and follicle-stimulating hormone
  9. Leydig cells and ovarian theca cells (the LH target)Sertoli cells and ovarian granulosa cells (the FSH target)
  10. GHRH and somatostatin (arcuate and periventricular nuclei)
  11. Somatotroph — growth hormone
  12. Hepatocyte — GH receptor and IGF-1 synthesis
  13. Tuberoinfundibular dopamine (prolactin-inhibiting factor)
  14. Supraoptic and paraventricular magnocellular neurones
  15. Lactotroph — prolactinPosterior pituitary — oxytocin release
  16. Mammary alveolus and myometrium
  17. CortisolThyroxine (T4) and triiodothyronine (T3)Testosterone and oestradiolInsulin-like growth factor 1Milk synthesis and the prolactin brake on GnRH
  18. Hypopituitarism and the order in which axes fail

Detail

Order of loss
GH, then LH and FSH, then TSH, then ACTH; prolactin deficiency is rare except in Sheehan syndrome, where failure to lactate is the first clue
Causes
Macroadenoma and its surgery or radiotherapy, craniopharyngioma, Sheehan syndrome, apoplexy, traumatic brain injury, hypophysitis including checkpoint inhibitor disease, sarcoidosis, haemochromatosis, empty sella
Replacement order
Hydrocortisone before levothyroxine — thyroxine raises cortisol clearance and metabolic demand and can precipitate an adrenal crisis in an unrecognised ACTH-deficient patient
Monitoring
Trophic hormones are useless for titration here: follow free T4, morning testosterone or symptoms, and IGF-1

When it goes wrong

Craniopharyngioma in a child

Growth failure with bitemporal hemianopia and suprasellar calcification, often with vasopressin deficiency as well

Checkpoint inhibitor hypophysitis (ipilimumab)

Headache and fatigue with ACTH and TSH deficiency weeks into treatment; give hydrocortisone and screen for the other axes

Levothyroxine started before hydrocortisone in a panhypopituitary patient

Adrenal crisis with hypotension and hyponatraemia

Practise this structure

2 questions in the bank tagged Pituitary.